Connective tissue disease-associated pulmonary arterial hypertension: "Beijing style".
نویسندگان
چکیده
Patients with connective tissue disease (CTD)-associated pulmonary arterial hypertension (APAH) experience poorer outcomes than those with idiopathic PAH (IPAH) [1–6]. In the USA, patients with systemic sclerosis (SSc) are most commonly affected by CTD-APAH and have the worst survival [1]. Similarly, 74% of a large cohort with CTD-APAH in the UK had SSc, and these patients had poorer survival than those with systemic lupus erythematosus (SLE) or polymyositis/dermatomyositis [7].
منابع مشابه
Connective tissue disease-associated pulmonary arterial hypertension
Although rare in its idiopathic form, pulmonary arterial hypertension (PAH) is not uncommon in association with various associated medical conditions, most notably connective tissue disease (CTD). In particular, it develops in approximately 10% of patients with systemic sclerosis and so these patients are increasingly screened to enable early detection. The response of patients with systemic sc...
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ورودعنوان ژورنال:
- The European respiratory journal
دوره 44 4 شماره
صفحات -
تاریخ انتشار 2014